Hem/Onc Pathology Section 8- Hemolytic anemia (intrinsic causes)

TOPICS: Sickle cell disease, autosomal recessive, beta globin gene, Glu, Val, HbS, tetramers, malaria, extravascular hemolysis, jaundice, hepatosplenomegaly, vaso-occlusive crisis, dehydration, hypoxemia, acidosis, dactylitis, avascular necrosis, priapism, acute chest syndrome, parvovirus B19, aplastic crisis, splenic sequestration, renal papillary necrosis, autosplenectomy, encapsulated organisms, sickle cell trait, sickled RBCs, target cells, Howell Jolly bodies, haptoglobin, hemoglobinemia, hemoglobinuria, crew cut skull, metabisulfite screen, hydroxyurea, HbF, pneumococcal vaccine, hereditary spherocytosis, ankyrin, spectrin, band 3, protein 4.2, spherocytes, splenic macrophages, MCHC, RDW, osmotic fragility test, eosin 5 maleimide binding test, splenectomy, G6PD deficiency, glutathione, NADPH, fava beans, sulfa drugs, primaquine, dapsone, haptoglobin, hemoglobinuria, LDH, unconjugated bilirubin, Heinz bodies, bite cells, pyruvate kinase deficiency, pyruvate kinase, glycolysis, ATP, 2,3 BPG, echinocytes, burr cells, paroxysmal nocturnal hemoglobinuria, PIGA gene, GPI, DAF, CD55, MIRL, CD59, episodic intravascular hemolysis, coombs negative hemolytic anemia, sucrose lysis test, flow cytometry, eculizumab, HbC disease, Glu, Lys, HbC crystals



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